Hemochromatosis

Home Alignment 1A6Z

1DE4 

METAL TRANSPORT INHIBITOR/RECEPTOR HEMOCHROMATOSIS PROTEIN HFE COMPLEXED WITH TRANSFERRIN RECEPTOR

1DE4 Metal Transport Inhibitor Receptor    
title Hemochromatosis Protein Hfe Complexed With Transferrin Receptor
   
compound source
Molecule: Hemochromatosis Protein
Chain: A, D, G
Fragment: Ectodomain
Synonym: Hfe
Engineered: Yes
Organism_scientific: Homo Sapiens
Organism_common: Human
Expression_system: Cricetulus Griseus
Expression_system_common: Chinese Hamster
Expression_system_cell: Ovary Cells
Expression_system_plasmid: Pbj5-Gs

Molecule: Beta-2-Microglobulin
Chain: B, E, H
Engineered: Yes

Organism_scientific: Homo Sapiens
Organism_common: Human
Expression_system: Cricetulus Griseus
Expression_system_common: Chinese Hamster
Expression_system_cell: Ovary Cells

Molecule: Transferrin Receptor
Chain: C, F, I
Fragment: Ectodomain
Engineered: Yes

Organism_scientific: Homo Sapiens
Organism_common: Human
Expression_system: Trichoplusia Ni
Expression_system_common: Cabbage Looper
Expression_system_cell: High 5 Insect Cells
Expression_system_plasmid: Pacgp67a
symmetry Space Group: C 1 2 1
R_factor 0.231
crystal
cell
length a length b length c angle alpha angle beta angle gamma
110.400 144.400 327.100 90.00 93.60 90.00
method X-Ray Diffraction resolution 2.80 Å
ligand NAG, CA, CRY enzyme
note 1DE4 is a representative structure
related structures by homologous chain: 1A6Z
 
MODEL STRUCTURE FOR 1DE4

1de4

MUTANT HFE PROTEIN

mutant HFE Protein


NORMAL HFE PROTEIN

normal HFE Protein